{"id":2117,"date":"2022-07-22T16:57:35","date_gmt":"2022-07-22T14:57:35","guid":{"rendered":"https:\/\/t21learning.institutlejeune.org\/?p=2117"},"modified":"2023-11-22T17:33:27","modified_gmt":"2023-11-22T16:33:27","slug":"hemosiderosis-pulmonarn-mucoviscidosis-y-trisomia-21","status":"publish","type":"post","link":"https:\/\/t21learning.institutlejeune.org\/es\/hemosiderosis-pulmonarn-mucoviscidosis-y-trisomia-21\/","title":{"rendered":"Hemosiderosis pulmonarn, mucoviscidosis y trisomia 21"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-post\" data-elementor-id=\"2117\" class=\"elementor elementor-2117\" data-elementor-post-type=\"post\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-b719a0f elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"b719a0f\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-207f4d3\" data-id=\"207f4d3\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d359a6a elementor-widget elementor-widget-text-editor\" data-id=\"d359a6a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>PATOLOG\u00cdAS RESPIRATORIAS<\/strong><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-29977f6 elementor-widget elementor-widget-heading\" data-id=\"29977f6\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Hemosiderosis pulmonar, mucoviscidosis y trisomia 21 <\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-8ad34f3 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"8ad34f3\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-66 elementor-top-column elementor-element elementor-element-41867bc\" data-id=\"41867bc\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-dcb356f elementor-widget elementor-widget-image\" data-id=\"dcb356f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img fetchpriority=\"high\" decoding=\"async\" width=\"932\" height=\"572\" src=\"https:\/\/t21learning.institutlejeune.org\/wp-content\/uploads\/2022\/03\/Pathologies_respiratoires_rares_associees.jpeg\" class=\"attachment-large size-large wp-image-2114\" alt=\"\" srcset=\"https:\/\/t21learning.institutlejeune.org\/wp-content\/uploads\/2022\/03\/Pathologies_respiratoires_rares_associees.jpeg 932w, https:\/\/t21learning.institutlejeune.org\/wp-content\/uploads\/2022\/03\/Pathologies_respiratoires_rares_associees-300x184.jpeg 300w, https:\/\/t21learning.institutlejeune.org\/wp-content\/uploads\/2022\/03\/Pathologies_respiratoires_rares_associees-768x471.jpeg 768w\" sizes=\"(max-width: 932px) 100vw, 932px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-e8fd8df\" data-id=\"e8fd8df\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-260a7d9 elementor-widget elementor-widget-toggle\" data-id=\"260a7d9\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"toggle.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-3981\" class=\"elementor-tab-title\" data-tab=\"1\" role=\"button\" aria-controls=\"elementor-tab-content-3981\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">ESQUEMA DEL CAPITULO<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-3981\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"1\" role=\"region\" aria-labelledby=\"elementor-tab-title-3981\"><p><a href=\"https:\/\/t21learning.institutlejeune.org\/es\/retrato-general-de-las-patologias-respiratorias-en-trisomia-21\/\" target=\"_blank\" rel=\"noopener\">1- Retrato general<\/a><\/p><p>\u00a0<\/p><p><a href=\"https:\/\/t21learning.institutlejeune.org\/es\/patologias-no-infecciosas-de-las-vias-aereas-superiores\/\" target=\"_blank\" rel=\"noopener\">2- Patolog\u00edas no infecciosas de las v\u00edas a\u00e9reas superiores<\/a><\/p><p>\u00a0<\/p><p><a href=\"https:\/\/t21learning.institutlejeune.org\/es\/patologias-no-infecciosas-del-pulmon-y-de-las-vias-aereas-inferiores\/\" target=\"_blank\" rel=\"noopener\">3- Patolog\u00edas no infecciosas del pulm\u00f3n y de las v\u00edas a\u00e9reas inferiores<\/a><\/p><p>\u00a0<\/p><p><a href=\"https:\/\/t21learning.institutlejeune.org\/es\/patologias-respiratorias-infecciosas-de-las-vias-aereas-superiores-vas\/\" target=\"_blank\" rel=\"noopener\">4- Patolog\u00edas respiratorias infecciosas de las v\u00edas a\u00e9reas superiores<\/a><\/p><p>\u00a0<\/p><p><a href=\"https:\/\/t21learning.institutlejeune.org\/es\/patologias-infecciosas-de-las-vias-respiratorias-bajas-en-las-personas-con-trisomia-21\/\">5- Patolog\u00edas infecciosas de las v\u00edas respiratorias bajas<\/a><\/p><p>\u00a0<\/p><p><a href=\"https:\/\/t21learning.institutlejeune.org\/es\/prevencion-de-las-infecciones-respiratorias\/\" target=\"_blank\" rel=\"noopener\">6- Prevenci\u00f3n de las infecciones respiratorias<\/a><\/p><p>\u00a0<\/p><p><a href=\"https:\/\/t21learning.institutlejeune.org\/es\/el-sindrome-de-apneas-obstructivas-del-sueno-saos\/\">7- El s\u00edndrome de apnea obstructiva del sue\u00f1o (SAOS)<\/a><\/p><p>\u00a0<\/p><p><a href=\"https:\/\/t21learning.institutlejeune.org\/es\/apneas-centrales-del-sueno-hipoventilacion-alveolar-e-hipoxemia\/\">8- Apnea central del sue\u00f1o, hipoventilaci\u00f3n alveolar e hipoxemia<\/a><\/p><p>\u00a0<\/p><p><strong><a href=\"https:\/\/t21learning.institutlejeune.org\/es\/hemosiderosis-pulmonarn-mucoviscidosis-y-trisomia-21\/\">9- Hemosiderosis pulmonar, mucoviscidosis y trisomia 21<\/a><\/strong><\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-122386f elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"122386f\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-8ad00be\" data-id=\"8ad00be\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-5564990 elementor-widget elementor-widget-spacer\" data-id=\"5564990\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-f8c47a1 elementor-widget elementor-widget-text-editor\" data-id=\"f8c47a1\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>La trisom\u00eda 21 se puede\u00a0 asociar con la mucoviscidosis (fibrosis qu\u00edstica),\u00a0 y con la hemosiderosis pulmonar. Estas dos patolog\u00edas pulmonares son muy raras, pero se deben conocer bien.<\/p><p>El doctor Herv\u00e9 Walti, pediatra en el Instituto J\u00e9r\u00f4me Lejeune, nos cuenta m\u00e1s detalles en este v\u00eddeo y la ficha t\u00e9cnica que le acompa\u00f1a, sobre los modos de presentaci\u00f3n a menudo at\u00edpicos que retrasan potencialmente el diagn\u00f3stico, su evoluci\u00f3n mas severa y su tratamiento m\u00e9dico, que debe ser el mismo que el de los pacientes neurot\u00edpicos.<\/p><p>\u00a0<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-f16d585 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"f16d585\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-3905d11\" data-id=\"3905d11\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7143697 elementor-widget elementor-widget-video\" data-id=\"7143697\" data-element_type=\"widget\" data-e-type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/youtu.be\\\/ROdV6JX1Xxw&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-b92c290 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"b92c290\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-b3df619\" data-id=\"b3df619\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-ebcec97 elementor-widget elementor-widget-spacer\" data-id=\"ebcec97\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-4a3e64c elementor-align-center elementor-widget elementor-widget-button\" data-id=\"4a3e64c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"button.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-button-wrapper\">\n\t\t\t\t\t<a class=\"elementor-button elementor-button-link elementor-size-sm\" href=\"https:\/\/t21learning.institutlejeune.org\/wp-content\/uploads\/2023\/08\/2.9-Patologias-pulmonares-raras-asociadas-a-la-trisomia-21-ES.pdf\" target=\"_blank\">\n\t\t\t\t\t\t<span class=\"elementor-button-content-wrapper\">\n\t\t\t\t\t\t\t\t\t<span class=\"elementor-button-text\">Descargar la ficha de s\u00edntesis<\/span>\n\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/a>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-0eb81e6 elementor-widget elementor-widget-spacer\" data-id=\"0eb81e6\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-2b0ab84 elementor-widget elementor-widget-shortcode\" data-id=\"2b0ab84\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"shortcode.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-shortcode\"><div class=\"_df_book df-lite\" id=\"df_3055\"  _slug=\"2-9-hemosiderosis-pulmonarn-mucoviscidosis-y-trisomia-21-_-esp\" data-title=\"2-9-hemosiderosis-pulmonarn-mucoviscidosis-y-trisomia-21-_-esp\" wpoptions=\"true\" thumbtype=\"\" ><\/div><script class=\"df-shortcode-script\" nowprocket type=\"application\/javascript\">window.option_df_3055 = {\"outline\":[],\"autoEnableOutline\":\"false\",\"autoEnableThumbnail\":\"false\",\"overwritePDFOutline\":\"false\",\"direction\":\"1\",\"pageSize\":\"0\",\"source\":\"https:\\\/\\\/t21learning.institutlejeune.org\\\/wp-content\\\/uploads\\\/2022\\\/07\\\/9.-Pathologies-respiratoires-rares-associees-__ES_relu.pdf\",\"wpOptions\":\"true\"}; if(window.DFLIP && window.DFLIP.parseBooks){window.DFLIP.parseBooks();}<\/script>\n<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-1e72e5a elementor-widget elementor-widget-spacer\" data-id=\"1e72e5a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-0558533 elementor-align-justify btn-refs elementor-widget elementor-widget-button\" data-id=\"0558533\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"button.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-button-wrapper\">\n\t\t\t\t\t<a class=\"elementor-button elementor-button-link elementor-size-sm\" href=\"#\">\n\t\t\t\t\t\t<span class=\"elementor-button-content-wrapper\">\n\t\t\t\t\t\t\t\t\t<span class=\"elementor-button-text\">Ver las referencias<\/span>\n\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/a>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<section class=\"elementor-section elementor-inner-section elementor-element elementor-element-aa2f110 div-refs div-refs-closed elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"aa2f110\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-inner-column elementor-element elementor-element-dba4f4e\" data-id=\"dba4f4e\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-f4f74b0 elementor-widget elementor-widget-text-editor\" data-id=\"f4f74b0\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>Alimi A, Taytard J, Abou Taam R, Houdouin V, Forgeron A, Lubrano Lavadera M, Cros P, Gibertini I, Derelle J, Deschildre A, Thumerelle C, Epaud R, Reix P, Fayon M, Roullaud S, Troussier F, Renoux MC, de Blic J, Leyronnas S, Thouvenin G, Perisson C, Ravel A, Clement A, Corvol H, Nathan N; French RespiRare\u00ae group. Pulmonary hemosiderosis in children with Down syndrome: a national experience. Orphanet J Rare Dis. 2018 Apr 20;13(1):60. doi: 10.1186\/s13023-018-0806-6. PMID: 29678139; PMCID: PMC5910623.<\/li><li>Bear CE. A Therapy for Most with Cystic Fibrosis. Cell. 2020 Jan 23;180(2):211. doi: 10.1016\/j.cell.2019.12.032. PMID: 31978337.<\/li><li>Bloom JL, Frank B, Weinman JP, Galambos C, O&#8217;Leary ST, Liptzin DR, Fuhlbrigge RC. Diffuse alveolar hemorrhage in children with trisomy 21. Pediatr Rheumatol Online J. 2021 Jul 17;19(1):114. doi: 10.1186\/s12969-021-00592-4. PMID: 34273981; PMCID: PMC8285855.<\/li><li>Bush D, Abman SH, Galambos C. Prominent Intrapulmonary Bronchopulmonary Anastomoses and Abnormal Lung Development in Infants and Children with Down Syndrome. J Pediatr. 2017 Jan;180:156-162.e1. doi: 10.1016\/j.jpeds.2016.08.063. Epub 2016 Sep 22. PMID: 27666181.<\/li><\/ul><ul><li>Bush D, Galambos C, Dunbar Ivy D. Pulmonary hypertension in children with Down syndrome. Pediatr Pulmonol. 2021 Mar;56(3):621-629. doi: 10.1002\/ppul.24687. Epub 2020 Feb 12. PMID: 32049444.<\/li><li>Charbek E, Kamel G, Nayak RP. Ivacaftor for the Treatment of Cystic Fibrosis Coexisting with Trisomy 21: A Case Report. Cureus. 2019 Nov 18;11(11):e6179. doi: 10.7759\/cureus.6179. PMID: 31890385; PMCID: PMC6919948.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-inner-column elementor-element elementor-element-fb356ba\" data-id=\"fb356ba\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-551e00b elementor-widget elementor-widget-text-editor\" data-id=\"551e00b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>Galambos C, Minic AD, Bush D, Nguyen D, Dodson B, Seedorf G, Abman SH. Increased Lung Expression of Anti-Angiogenic Factors in Down Syndrome: Potential Role in Abnormal Lung Vascular Growth and the Risk for Pulmonary Hypertension. PLoS One. 2016 Aug 3;11(8):e0159005. doi: 10.1371\/journal.pone.0159005. PMID: 27487163; PMCID: PMC4972384.<\/li><li>Guy EL, Peckham DG, Brownlee KG, Conway SP, Lee TW. Cystic fibrosis co-existing with trisomy 21. J Cyst Fibros. 2010 Sep;9(5):330-1. doi: 10.1016\/j.jcf.2010.05.003. Epub 2010 Jun 11. PMID: 20538528.<\/li><li>Milunsky A. Cystic fibrosis and Down&#8217;s syndrome. Pediatrics. 1968 Sep;42(3):501-4. PMID: 4234128.<\/li><li>Ruf K, Demerath A, Hebestreit H, Kunzmann S. Is sweat testing for cystic fibrosis feasible in patients with down syndrome? BMC Pulm Med. 2018 Jan 16;18(1):8. doi: 10.1186\/s12890-018-0580-1. PMID: 29338740; PMCID: PMC5771200.<\/li><li>Tobai H, Yano J, Sato N, Amanuma F, Takahashi M, Endo M, Ishimura M, Ohga S, Maruyama H. Successful Liposteroid Therapy for a Recurrent Idiopathic Pulmonary Hemosiderosis with Down Syndrome. Case Rep Pediatr. 2020 Apr 25;2020:5292947. doi: 10.1155\/2020\/5292947. 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